Renal--skeletal--ear- and facial-anomalies in combination with the Mayer--Rokitansky--Küster (MRK) syndrome.

نویسنده

  • W N Willemsen
چکیده

The combination of the Mayer--Rokitansky--Küster (MRK) syndrome with renal anomalies is well known (incidence: 36%). The combination with skeletal anomalies is also known (incidence: 10%). However, the coincidence with ear anomalies is rare, and the coincidence with facial anomalies is extremely rare. The combination of the MRK syndrome with renal, skeletal, ear and facial anomalies is described in a case report with a review of the literature. It is not only worthwhile to be alert for urinary tract anomalies in patients with the MRK syndrome, but also to study the skeletal and auditory systems in these patients.

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عنوان ژورنال:
  • European journal of obstetrics, gynecology, and reproductive biology

دوره 14 2  شماره 

صفحات  -

تاریخ انتشار 1982